Dermatofibrosarcoma protuberans is a slow-growing, locally aggressive,
fibrous tumor that, on rare occasions, metastasizes to distant sites
or regional lymph nodes. We have found 28 patients with metastasis in
the literature; 9 of these patients had lymph node metastasis. In this
report we present a case of dermatofibrosarcoma protuberans of the lo
wer extremity with metastasis to inguinal lymph nodes appearing 10 mon
ths after wide excision and skin grafting of the primary lesion. The c
linical and pathological features of this case are presented. Although
, along with our patient, 10 cases of regional lymph node metastasis a
re not justification for regional lymph node dissections, they do emph
asize the need for regional lymph node examinations in the long-term f
ollow-up of dermatofibrosarcoma protuberans cases.