Blau's syndrome is a familial multisystem granulomatous inflammation w
hich may be confused with childhood sarcoidosis because it presents wi
th iridocyclitis, posterior uveitis, granulomatous skin disease, arthr
itis and elevated serum angiotensin-converting enzyme. They are distin
guished by the absence of pulmonary involvement and a negative Kveim-S
iltzbach skin test.