Two patients developed unilateral occipitotemporal infarcts that produ
ced inferior quadrantic achromatopsia and an accompanying superior qua
drantanopia. Magnetic resonance imaging and single-photon emission com
puted tomographic studies of both patients supported the current view
that color vision is encoded in the lingual and fusiform gyri. Althoug
h the quadrantic defect in color processing was profound, neither pati
ent was aware of it. Simple bedside testing of patients with superior
quadrantanopia may disclose an unrecognized quadrantic achromatopsia.