Xanthogranuloma (XG) is a rare disease in adults. The authors report a
case of XG in an 20 years-old woman. This observation is particulary
interesting: First by the pathology of the cutaneous lesion which show
ed a dermal infiltrate composed of histiocytes and a few foamy cells b
ut without Touton giant cells. Second by is association with a mastocy
tosis which disappeared when XG appeared. These data led the authors t
o discuss the misleading histology pattern of XG and also the pathogen
esis of XG. In our case. it would appeared as a benign reactive proces
s against mastocytosis.