Thirty-eight cases of Larsen's syndrome were analyzed with an average
follow-up of 13 years. Knee deformities were classified according to L
eveuf and Pais grades: 12 patients had a grade 1 tibiofemoral dislocat
ion, five had a grade two, and 18 had a grade 3. Six patients had isol
ated dislocations or subluxations of the patella. Fourteen patients wi
th 22 unstable knees were surgically treated. This series supports the
idea of early treatment of knee problems, with an open procedure for
grade 3 (resection of medial and lateral retinacula and iliotibial fas
cia, V-Y reconstruction of the extensor apparatus, suture of the media
l plane, medial transfer of one-third of the patellar tendon, capsulor
aphy, tibiofermoral pinning, and plaster cast). Performing surgery on
grade 2 dislocations is worthwhile only when they are accompanied by p
atelofemoral dislocations. If they are grade 1, progressive casting in
flexion is justified. Patellofemoral dislocations should be operated
on early. Dislocatable patellas should be treated only if they interfe
re with function.