Glomerulonephritis complicating primary Gougerot-Sjogren's syndrome is
extremely rare. We report the case of a 72-year old woman with primar
y Gougerot-Sjogren syndrome complicated by progressive renal failure.
Kidney biopsy revealed a crescentic glomerulonephritis. A rapid improv
ement occurred with corticosteroids. This observation is, at our knowl
edge, the first case of crescentic glomerulonephritis described during
this disease. A review of the literature concerning glomerulonephriti
s complicating primary Gougerot-Sjogren syndrome is reported.