This report describes what the authors believe to be the first reporte
d case of choristoma of the intracranial maxillary nerve. This 12-year
-old girl presented with a 5-year history of severe isolated left-side
d trigeminal neuralgia. Computerized tomography and magnetic resonance
imaging revealed a mass below the anterior portion of the left cavern
ous sinus, enlarging the foramen rotundum. Total resection was achieve
d via a pterional extradural approach. Histological examination reveal
ed a choristoma composed of smooth-muscle fibers. The histogenesis of
these tumors when they develop in a nerve remains unclear. They may re
present abnormal migration or proliferation of neuroectodermal tissue
in or close to a peripheral nerve. Total removal of these tumors shoul
d be attempted at initial diagnosis.