PARTIAL ANOMALOUS PULMONARY VENOUS DRAINAGE ASSOCIATED WITH INTACT ATRIAL SEPTUM AND PULMONARY VALVE STENOSIS

Partial anomalous pulmonary venous drainage (PAPVD) with an intact atr ial septum is a very rare cardiovascular anomaly. Most PAPVD cases can be detected by echocardiographic scanning of the anomalous pulmonary venous connection. This paper describes an asymptomatic 6-year-old boy who was referred because of a heart murmur. An electrocardiogram and two-dimensional echocardiography revealed right heart volume overload. Mild pulmonary valve stenosis and an intact atrial septum were noted. In addition, color flow mapping demonstrated the right upper pulmonar y vein connecting to the superior vena cava. This paper emphasizes tha t two-dimensional echocardiography in conjunction with color flow mapp ing isa valuable modality in the detection of anomalous pulmonary veno us drainage.