CASE-REPORT - PERINEPHRIC ANGIOMYOLIPOMAS IN TUBEROUS SCLEROSIS

Bilateral large perinephric angiomyolipomas in a young Chinese woman w ith tuberous sclerosis are reported. Computed tomography (CT) demonstr ated large fatty masses, containing abnormally dilated blood vessels a nd muscle strands, within the Gerota's fascia bilaterally. There were multiple foci of involvement in both kidneys. The diagnosis was confir med on histological examination of the excised left perinephric angiom yolipoma and nephrectomy specimens. The patient subsequently developed bilateral pneumothoraces which were surgically treated. High resoluti on CT showed extensive thin-walled cysts in both lungs.