A 5-year-old girl had pemphigus erythematosus based on clinical and im
munohistologic criteria. The rare occurrence in childhood of the pemph
igus group of disorders, and of pemphigus erythematosus in particular,
is discussed. We also review current knowledge concerning the delinea
tion of the different pemphigus subsets and the treatment of pemphigus
erythematosus.