EEG EVALUATION OF CHILDREN WITH STURGE-WEBER SYNDROME AND EPILEPSY

To define the contribution of the EEG evaluation in children with seiz ures and Sturge-Weber syndrome, we reviewed EEG data in 14 radiologica lly confirmed cases. Thirteen exhibited marked voltage attenuation tha t was localized to the region of the cerebral angiomatosis. Polymorphi c slowing occurred ipsilateral to the lesion in six patients and was b ilateral in six. By contrast, interictal spikes were evident in only t wo patients and did not always correlate with the angiomatosis. Seizur es were captured in four patients and consistently revealed ictal disc harges only at the periphery of the lesion. These findings indicate th at abnormalities of EEG background rather than interictal spikes are c onsistently present early in the course of Sturge-Weber syndrome and c orrelate with the region of angiomatosis.