During the nine-year period from 1983 to 1991, a total of 242 patients
(142 males and 100 females) presenting with Kawasaki disease were see
n at one hospital. Among them, 25 (10%) patients demonstrated incomple
te Kawasaki disease and 17 of these 25 (68%) lacked two of the six pri
ncipal symptoms of Kawasaki disease, with the most frequently missing
symptoms being cervical lymphadenopathy and polymorphous exanthema. Th
e typical laboratory features of Kawasaki disease, such as elevated er
ythrocyte sedimentation rate, leukocytosis, anemia, positive C-reactiv
e protein and thrombocytosis were also seen in the incomplete cases. N
one of the 25 patients underwent iv gamma-globulin therapy while in 1
(4%), transient dilatation of the coronary artery was recognized. Inco
mplete Kawasaki disease may therefore be characterized by a less frequ
ent association of rash, cervical lymphadenopathy and coronary involve
ment.