An infant with intrathoracic extra-mediastinal cystic hygroma is descr
ibed. Fluid collection within the fetal chest was noted on routine ant
enatal ultrasound scan and this was subsequently drained. Postnatally,
echocardiogram and thoracic CT scan demonstrated a cystic space betwe
en the pericardium and right mediastinal pleura. Thoracotomy performed
at six weeks of age showed a multiloculated cystic mass adherent to t
he right pericardium and to the medial aspect of the diaphragm. Histol
ogy revealed the tumour to be a cystic hygroma (lymphangioma). Intrath
oracic cystic hygroma occurring outside the mediastinum is extremely r
are and has never been diagnosed previously in infancy.