JUVENILE ARTERIOSCLEROSIS - RARE CAUSE OF A GENERALIZED DILATATIVE AND STENOSING VASCULAR-DISEASE

In addition to generalized arteriosclerosis connective tissue disease, systemic vasculitis as well as genetic metabolic disease are describe d to be the cause of stenotic and aneurysmatic vessel wall alteration. Although these causes are rather unusual, they must be considered for the diagnosis of a generalized vascular disease with arterial occlusi on as well as aneurysm formation to determine the appropriate procedur e for the individual. Whereas operative treatment should be avoided as far as possible for patients with Behcet's disease or Marfan syndrome , it is rather indicated for any kind of juvenile arteriosclerosis wit h arterial stenosis as well as dilatation. In this way the patient des cribed in the following could be treated successfully by operation eve n though the cause of the juvenile arteriosclerosis was inexplicable, and in addition to local complications also the threatening rupture of the aneurysm could be controlled.