APLASIA-CUTIS-CONGENITA - NEW EVIDENCE SUPPORTING THE AMNIOTIC BAND THEORY OF ORIGIN

We present two cases of aplasia cutis congenita (ACC). The scalp alone was involved in the first baby, who died from massive sagittal sinus hemorrhage. The second neonate presented with circumferential constric tive trunk ulcers and healed scars on the thighs, axillae, and temples in addition to the scalp lesion. This baby was successfully treated w ith local flap cover of the scalp and trunk ulcers. A biopsy from the edge of the scalp ulcer revealed a dermoid cyst. This provides new evi dence in support of the amniotic band theory of origin of ACC.