A congenital defect of the scrotal wall with consequent testicular exs
trophy is an exceptional finding. The etiopathogenesis of this defect
is debated. We report a newborn male with arthrogryposis who presented
with an exstrophied testicle. The association of these two conditions
seems to establish a cause-effect relationship mediated by mechanical
factors, i.e., in utero compression of the scrotum by the feet. It is
likely that a similar mechanism could also be advocated to explain th
e previous cases reported in the literature.