Background. - Congenital origin of brain fibrolipoma is still debated.
A case of such a tumor is presented. Case report. - A female newborn
presented with severe hypotonia and macrocephaly that were seen since
birth. She died at the age of 2 days. Post-mortem examination showed h
ydrocephaly due to a tumor located in the mesencephalo-protuberantial
region. Histological features of this tumor were those of a fibrolipom
a. Conclusion. - The presence of this brainstem tumor at birth confirm
s its congenital origin.