HASHIMOTO-PRITZKER RETICULOHISTIOCYTOSIS AND CONGENITAL HISTIOCYTOSIS

Background. - Congenital histiocytosis is divided bite four entities d iffering in their clinical and histological features and prognosis. Ea rly; accurate diagnosis is essential Sor treatment. Case report. - Sev en cutaneous nodules were seen in a male neonate. One of these nodules was biopsied on the 7th day of life; it showed the typical finds of H ashimoto-Pritzker reticulohistiocytosis by optical and electron micros copy using immunological markers. The nodules spontaneously disappeare d after a few months. Conclusion. - Congenital forms of histiocytosis must be accurately characterized. Hashimoto-Pritzker reticulohistiocyt osis is a benign and self-healing disease restricted to the skin, whil e the Letterer-Siwe disease has a completely different course and trea tment.