Fifteen cases of desmoplastic melanocytic naevi are described in 12 fe
male and three male patients, ranging in age from 8 to 8 3 years. The
commonest site for the lesions was the upper limb. The lesions were ch
aracterized by a dense sclerotic or desmoplastic appearance of the der
mal collagen surrounding a population of predominantly epithelioid nae
vus cells, some of which had a bizarre but non-malignant cytology. The
cause of the stromal change is not established. We suggest that these
lesions constitute a discrete entity which should be described in sta
ndard textbooks of dermatopathology.