SURGERY FOR CONGENITAL-MALFORMATIONS OF THE LUNG

In the course of a survey conducted in 59 hospitals performing thoraci c surgery, 14 hospitals supplied data that could be used for the study . Out of 1347 anomalies diagnosed 1343 were surgically treated, with a 30-day mortality rate of 0.3% (5 patients). In a retrospective study over a period of 10 years (1978-1988) we identified 198 anomalies out of a total of 6350 thoracotomies ; so our percentage grading of pulmon ary anomalies is supported by the data of the above-mentioned survey a ccording to which cystic pulmonary malformations such as inhibition ma lformations, excess malformation and lobar emphysema represent a major ity with 72.2% (survey 83%). Congenital anomalies of lung formation oc curred in 23% of the patients of the survey and in 15% of our own pati ents. Therapy consisted of parenchyma-saving surgery, i.e. enucleation (n = 87), segmental resection (n = 65) and lobectomy (n = 63) with br onchoplastic reconstruction; there was no 30-day mortality. Adenomatoi d-cystic malformation, lymphangiectasis, congenital lobar emphysema an d stenosis of the tracheobronchial tree are often an indication for im mediate surgical treatment in neonates. Solitary cysts, bronchiectasis , sequestration of the lung, an AV-fistula present with symptoms mostl y between the ages of 20-40 and therefore were surgically treated seco ndarily.