SYSTEMIC AMYLOIDOSIS IN A PATIENT WITH ADULT ONSET STILLS DISEASE

A 39-year-old woman presented clinical features of adult onset Still's disease. Seven years after the onset, she developed renal insufficien cy and biopsy studies revealed amyloid deposits involving amyloid A pr otein, P component, lambda chain and kappa chain in the kidney and rec tum. She died in 1992, primarily due to cardiac failure associated wit h amyloidosis, indicating that amyloidosis should be considered one of the fatal complications in adult onset Still's disease with a long hi story.