A KINDRED OF HEREDITARY ADULT-ONSET LEUKODYSTROPHY WITH SPARING OF THE OPTIC RADIATIONS

Authors
ABE K IKEDA M WATASE K TANABE H FUJIMURA H YORIFUJI S UENO S MEZAKI T MORI T
Citation
K. Abe et al., A KINDRED OF HEREDITARY ADULT-ONSET LEUKODYSTROPHY WITH SPARING OF THE OPTIC RADIATIONS, Neuroradiology, 35(4), 1993, pp. 281-283
Citations number
8
Journal title
Neuroradiology → ACNP
ISSN journal
00283940
Volume
35
Issue
4
Year of publication
1993
Pages
281 - 283
Database
ISI
SICI code
0028-3940(1993)35:4<281:AKOHAL>2.0.ZU;2-X
Abstract
We describe a family with hereditary adult-onset leukodystrophy with s paring of the optic radiations, shown clinically, neuroradiologically and electrophysiologically. All five affected members developed their leukodystrophy in their fourth decade and clinical features steadily p rogressed. The sparing of the optic radiations is not typical of other leukodystrophies. We suggest that this is a new clinical entity.