SECUNDARY ARTERIAL-HYPERTENSION IN TYPE-INEUROFIBROMATOSIS (NF-1) - FINDINGS IN 6 PATIENTS

With the aim to analyze the association of Type I Neurofibromatosis wi th secondary arterial hypertension, a retrospective study has been per formed on 36 patients, diagnosed of pheochromocytoma (n=12) and/or ren al artery stenosis (n=25), finding in 6 of them diagnostic criteria of Type I neurofibromatosis, of these 4 showed pheochromocytoma, 1 renal artery stenosis and 1 pheochromocytoma plus renal artery stenosis. CA T and angiography were the best diagnostic imaging methods to confirm clinic and biological suspicion of adrenal tumor o renal artery stenos is. It is recommended the systemized study of patients with NF-1 toget her with their relatives who phenotypically show some illness stigma, or with arterial hypertension resistant to conventional treatment.