OBSTETRIC AND ANESTHETIC CONSIDERATIONS IN THE MAY-HEGGLIN ANOMALY - A CASE-REPORT

The obstetric and anesthetic considerations in the management of a pat ient with the May-Hegglin anomaly, an autosomal dominant platelet defi ciency, are discussed. A review of the medical literature notes three previous case reports of May-Hegglin anomaly in pregnancy. In addition to the two successful pregnancies reported in this paper, there are f our infant survivors among the five reported pregnancies. Anesthetic m anagements included general and spinal anesthesia: the latter employed following platelet transfusion. A successful pregnancy should be anti cipated when management includes a well-informed patient and coordinat ed obstetric and anesthetic care.