The case of a combined intra- and extraspinal neurenteric cyst in an i
nfant is reported. This case is unique because an intraspinal cyst was
not suspected clinically until large numbers of squamous epithelial c
ells were obtained at lumbar puncture performed as part of a workup fo
r a septic entity. The cyst extended from an intradural location ventr
al to the conus medullar-is at L-1 through a ventrolateral defect in t
he S-4 vertebral body to communicate with a large presacral component.
The entire cystic cavity was lined by stratified squamous epithelium.
The possible pathogenesis of this lesion is discussed.