We report a case of fetal endocarditis coexisting with a congenital he
art defect: a common atrium (left atrial isomerism) with complete cong
enital heart block. The case was studied by echocardiography from 32 t
o 39 weeks of gestation. A postmortem examination was carried out a fe
w hours after Cesarean section. The autopsy, histopathological and imm
unohistochemical findings revealed endocarditis. We think that abnorma
l turbulent systolic and diastolic flow of the semilunar valve, seen i
n fetal Doppler echocardiography, may be a sign of fetal endocarditis
even though clear evidence of vegetations were not seen.