SCINTIGRAPHIC EVALUATION OF REDUCED-SIZE LIVER-TRANSPLANT FROM LIVING-RELATED DONOR IN BYLERS DISEASE

Byler's syndrome is a rare form of autosomal recessive intrahepatic ch olestasis that is fatal in children. A 10-year-old girl diagnosed with Byler's syndrome underwent reduced-size liver transplantation using l ateral segments of her living mother's liver. The donor's and the reci pient's liver functions after transplantation were evaluated using Tc- 99m disofenin and Tc-99m SC to investigate morphology, liver perfusion , and hepatobillary function.