DERMATOFIBROSIS-LENTICULARIS-DISSEMINATA WITH OSTEOPOIKILOSIS (BUSCHKE-OLLENDORF-SYNDROME

Buschke-Ollendorff syndrome is characterized by the coincidence of der matofibrosis lenticularis disseminata and focal sclerotic bone dysplas ia (osteopoikilosis). The case of a 39-year-old female is presented an d the characteristic clinical, histopathological and radiological mani festations of this rare disease are reviewed. As focal bone lesions in Buschke-Ollendorff's syndrome are mostly asymptomatic, the rate of di agnosis could be increased if locations of predilection were subjected to X-ray examinations on clinical observation of the typical cutaneou s manifestations.