FAMILIAL PROGRESSIVE SUPRANUCLEAR PALSY

Authors
BROWN J LANTOS P STRATTON M ROQUES P ROSSOR M
Citation
J. Brown et al., FAMILIAL PROGRESSIVE SUPRANUCLEAR PALSY, Journal of Neurology, Neurosurgery and Psychiatry, 56(5), 1993, pp. 473-476
Citations number
23
Categorie Soggetti
Psychiatry,Neurosciences,"Clinical Neurology
Journal title
Journal of Neurology, Neurosurgery and Psychiatry → ACNP
ISSN journal
00223050
Volume
56
Issue
5
Year of publication
1993
Pages
473 - 476
Database
ISI
SICI code
0022-3050(1993)56:5<473:FPSP>2.0.ZU;2-#
Abstract
A progressive extrapyramidal syndrome and dementia occurred in three m embers of one family. The age of onset was in the seventh decade and t he affected individuals showed many of the clinical features of progre ssive supranuclear palsy (PSP). Necropsy of one individual revealed th e neuropathological features of PSP. We propose that this family has a familial form of PSP and review the evidence in the literature that a familial form exists.