NEURONAL MIGRATIONAL DISORDERS - DIFFUSE CORTICAL DYSPLASIA OR THE DOUBLE CORTEX SYNDROME

We report a 10-year-old girl who presented with a single episode of pa rtial complex seizure. Neurological examination and psychological eval uation were normal. Electroencephalogram showed abnormalities in the l eft temporo-occipital region. Magnetic resonance imaging revealed a bi lateral layer of tissue iso-intense with gray matter, between the wall of the lateral ventricle and the cortex, extending from the frontal t o the occipital region, and enlarged left lateral ventricle. The image s indicated diffuse cortical dysplasia, also known as band heterotopia or ''double cortex'', and left cortical hemiatrophy.