KASABACH-MERRITT SYNDROME WITH PROFOUND PLATELET SUPPORT

Authors
HENLEY JD DANIELSON CFM ROTHENBERGER SS HSUEH Y THELIA A MCCARTHY LJ
Citation
Jd. Henley et al., KASABACH-MERRITT SYNDROME WITH PROFOUND PLATELET SUPPORT, American journal of clinical pathology, 99(5), 1993, pp. 628-630
Citations number
16
Categorie Soggetti
Pathology
Journal title
American journal of clinical pathology → ACNP
ISSN journal
00029173
Volume
99
Issue
5
Year of publication
1993
Pages
628 - 630
Database
ISI
SICI code
0002-9173(1993)99:5<628:KSWPPS>2.0.ZU;2-O
Abstract
The Kasabach-Merritt Syndrome describes thrombocytopenia occurring in patients with giant hemangiomata. The resultant thrombocytopenia may b e profound and occasionally even life-threatening. An 11-month-old inf ant with prolonged thrombocytopenia whose course was complicated by re current hemorrhaging requiring intense platelet transfusions is report ed. During her 19-month hospitalization she received 6,622 platelet co ncentrates. This represents the most extensive platelet support ever g iven to an infant with this syndrome.