DISCRETE SUBVALVULAR AORTIC-STENOSIS IN THE BECKWITH-WIEDEMANN SYNDROME

Authors
SHIRANI J NATARAJAN K VARGA P VITULLO DA
Citation
J. Shirani et al., DISCRETE SUBVALVULAR AORTIC-STENOSIS IN THE BECKWITH-WIEDEMANN SYNDROME, Pediatric cardiology, 14(3), 1993, pp. 194-195
Citations number
7
Categorie Soggetti
Cardiac & Cardiovascular System",Pediatrics
Journal title
Pediatric cardiology → ACNP
ISSN journal
01720643
Volume
14
Issue
3
Year of publication
1993
Pages
194 - 195
Database
ISI
SICI code
0172-0643(1993)14:3<194:DSAITB>2.0.ZU;2-D
Abstract
Various congenital cardiac malformations have been described in patien ts with Beckwith-Wiedemann (BW) syndrome, including reversible obstruc tive subaortic stenosis in one patient. We herein present a case of a 2.5-year-old black boy with BW syndrome and discrete subvalvular aorti c stenosis of the membraneous type. Such association of these two enti ties has previously not been documented.