MULTIFOCAL FIBROSCLEROSIS - REPORT OF A CASE OF BILATERAL IDIOPATHIC SCLEROSING PSEUDOTUMOR AND RETROPERITONEAL FIBROSIS

We describe a 56-year-old white man who presented with gradual and pro gressive visual loss and subsequent hypertension and pedal edema. A co mputed tomographic scan of the orbits showed bilateral diffuse retrobu lbar masses, and an abdominal computed tomographic scan showed a diff use retroperitoneal mass invading the aorta, Ureters, and inferior ven a cava. Biopsies of the orbit and abdomen confirmed a heterogeneous ce ll population and marked fibrosis consistent with a sclerosing inflamm atory process. Bilateral sclerosing orbital inflammatory disease shoul d cue the physician to suspect coexisting SYStemic disease. This repor t is the fourth to document bilateral sclerosing orbital inflammatory disease and the second to have obtained biopsies of the orbit and abdo men showing histologic similarities.