CONGENITAL HISTIOCYTOSIS-X

Congenital histiocytosis X involving multiple organs is a rare disease that causes rapid mortality in intrauterine and neonatal life. The di agnosis of histiocytosis X (Litterer-Siwe disease should be considered in a neonate with vesiculated crusting skin lesions. We present clini cal, radiographic and histopathological findings in a neonate with con genital histiocytosis who died of respiratory failure due to diffuse i nfilteration of lungs with histiocytic cells.