The ''crisscross'' heart and the heart with ''superoinferior ventricle
s'' are closely related congenital cardiac malformations that are char
acterized by twisted atrioventricular connections. The authors studied
the morphologic characteristics of three hearts with twisted atrioven
tricular connections as seen on magnetic resonance (MR) images. The mo
st important clue to the diagnosis was the distorted atrioventricular
connections that were demonstrated on serial images. The axes of the a
trioventricular connections through the atrioventricular valves were n
ot parallel to each other. The presence of unusual recesses in the car
diac chambers, the angulated or curved configuration of the atrial and
ventricular septa, and the unexpected great arterial relationship for
the given combination of segmental connections supported the findings
of twisted atrioventricular connections. MR imaging facilitated the p
recise morphologic diagnosis of these hearts.