BILATERAL ISOLATED RETROBULBAR OPTIC NEUROPATHY IN LIMITED WEGENERS GRANULOMATOSIS

Wegener's granulomatosis causes a variety of ophthalmologic disorders, some of which occasionally constitute the initial presentation of the disease. We describe a patient who presented with bilateral, isolated , consecutive, posterior optic neuropathy with light perception and no light perception vision. The patient had no other symptoms or signs o f orbital disease. Investigations revealed cavitary lung lesions, posi tive antineutrophilic cytoplasmic antibody (ANCA) titers, subtle focal enhancement of the intracanalicular optic nerves on magnetic resonanc e imaging, and a confirmatory bronchial biopsy. This exceedingly rare ocular presentation of Wegener's granulomatosis may pose a diagnostic quandary.