D. Roger et al., TYPE-IV EHLERS-DANLOS SYNDROME REVEALED BY ACUTE OBSTRUCTIVE RENAL-FAILURE, Annales de dermatologie et de venereologie, 120(5), 1993, pp. 387-389
A 64 year-old man was admitted for congestive heart failure induced by
an acute renal failure due to obstruction. Retroperitoneal periaortic
-aneurysmal fibrosis was the etiology of the obstruction. Type IV Elhe
rs-Danlos syndrome was diagnosed based upon clinical and histological
cutaneous signs.