We report the case of a pregnant woman suffering from pseudoxanthoma e
lasticum with typical cutaneous manifestations, arteritis of the lower
limbs and angioid striae. The course of pregnancy was marked by trans
ient inflection of the foetal growth curve with return to normal after
a few weeks of rest in hospital. Delivery was effected by caesarean s
ection in the 35th week of amenorrhoea; the placenta contained numerou
s calcifications. Two years after pregnancy, our patient experienced a
ggravation of skin lesions, but the arteritis and the ocular involveme
nt remained unchanged. These <<at risk>> pregnancies must be closely m
onitored.