HISTIOCYTOSIS-X AND SCLEROSING CHOLANGITIS

Authors
SOUA H POUSSE H LADEB F KORBI S AYADI A BOUSSOFFARA R BELKHIR Y DESCOS B SFAR MT HARBI A ESSOUSSI S
Citation
H. Soua et al., HISTIOCYTOSIS-X AND SCLEROSING CHOLANGITIS, Annales de pediatrie, 40(5), 1993, pp. 316-319
Citations number
NO
Categorie Soggetti
Pediatrics
Journal title
Annales de pediatrie → ACNP
ISSN journal
00662097
Volume
40
Issue
5
Year of publication
1993
Pages
316 - 319
Database
ISI
SICI code
0066-2097(1993)40:5<316:HASC>2.0.ZU;2-0
Abstract
The case of a seven-year-old with multifocal (type II) Langherans' cel l histiocytosis since the age of two years is reported. Despite therap y, biliary cirrhosis with portal hypertension developed gradually. His tologic studies of liver biopsy specimens, computed tomography, and tr anshepatic cholangiography disclosed dilatation of the bile ducts, sug gesting sclerosing cholangitis, a specific complication of Langherans' cell histiocytosis which precipitates the development of biliary cirr hosis.