We report a case of diffuse erythrodermic cutaneous mastocytosis with
bone marrow infiltration. An 11-month-old female patient was referred
to our hospital for intermittent flushing, fever, intense itching, ery
thematous rash and bullous lesions. Cutaneous biopsy demonstrated diff
use cutaneous mastocytosis. The bone marrow aspirate revealed mast cel
l infiltration. Ketotifen treatment was very effective.