Mw. Walker et al., MULTIPLE AREAS OF INTESTINAL ATRESIA ASSOCIATED WITH IMMUNODEFICIENCYAND POSTTRANSFUSION GRAFT-VERSUS-HOST DISEASE, The Journal of pediatrics, 123(1), 1993, pp. 93-95
We describe an infant with multiple segmental areas of atresia of the
small and large bowel, with histologic features characteristic of the
hereditary form of the disease. Posttransfusion graft-versus-host dise
ase developed first, and then immunodeficiency was found. This report
confirms the association between hereditary multiple intestinal atresi
a and immunodeficiency. We recommend irradiation of blood products in
patients with multiple intestinal atresia pending evaluation of immune
system status.