SPONTANEOUS SUBCLAVIAN ARTERY DISSECTION IN A TYPE-IV EHLERS-DANLOS SYNDROME

The authors report an unusual dissequant aneurysm of the left subclavi an artery occuring in a patient suffering from the Ehlers-Danlos syndr ome. Clinical history and skin biopsy permitted this diagnosis. Surgic al treatment associated resection of the aneurysm, ligation of the pro ximal part of the subclavian artery and a prosthetic bypass between ca rotid and subclavian artery. Spontaneous dissequant aneurysm is a rare disease and one must think before surgery to arterial dysplasia. Tech nical features of the surgical treatment are discussed (J Mal Vasc, 19 93, 18, pages 146-148).