Wa. Curtin et al., PIGMENTED VILLONODULAR SYNOVITIS ARISING FROM THE SHEATH OF THE EXTENSOR HALLUCIS-LONGUS IN AN 8-MONTH-OLD INFANT, Clinical orthopaedics and related research, (292), 1993, pp. 282-284
Pigmented villonodular synovitis (PVS) is a disease of unknown origin
that most commonly affects the synovial joints and synovial sheaths of
the skeletally mature. In an eight-month-old infant, a leg swelling t
hought likely to be a sarcoma proved to be PVS on biopsy.