ORGANIZATION AND RESULTS OF STUDIES ON AC UTE HEPATIC PORPHYRIAS IN POLAND

The organization, activities and experience of Porphyria Reference Cen tre of the Institute of Hematology in Poland is shown. A total of 214 families with acute hepatic porphyria were collected. The family studi es in search of latent cases were conducted, and measures for preventi ng the disease attacks were taken. The therapy of the attacks consiste d in glucose and heme arginate infusions, and hyperalimentation in the patients is stressed. The incidence rate of porphyrias in Poland, acc ording to the material collected at the Institute of Hematology is 1:1 5 000 inhabitants, however, it is suggested that the true value is muc h higher.