UNDIFFERENTIATED SOFT-TISSUE TUMOR WITH R HABDOID PHENOTYPE - (EXTRA RENAL RHABDOID TUMOR) - A CONGENITAL CASE ASSOCIATED WITH MEDULLOBLASTOMA IN A BROTHER

Authors
COSTES V MEDIONI D DURAND L SARRAN N MARGUERITE G BALDET P
Citation
V. Costes et al., UNDIFFERENTIATED SOFT-TISSUE TUMOR WITH R HABDOID PHENOTYPE - (EXTRA RENAL RHABDOID TUMOR) - A CONGENITAL CASE ASSOCIATED WITH MEDULLOBLASTOMA IN A BROTHER, Annales de pathologie, 17(1), 1997, pp. 41-43
Citations number
10
Categorie Soggetti
Pathology
Journal title
Annales de pathologie → ACNP
ISSN journal
02426498
Volume
17
Issue
1
Year of publication
1997
Pages
41 - 43
Database
ISI
SICI code
0242-6498(1997)17:1<41:USTWRH>2.0.ZU;2-2
Abstract
We report a case of congenital cervical rhabdoid tumor, with associati on of a medulloblastoma in a brother. The immunohistochemical features of this tumor are compatible,vith a neuroectodermal differenciation ( MIG 2+, Leu 7+). Extrarenal rhabdoid tumors share a common morphology but do not represent a single entity with only one histogenesis. Most of them are now considered to be of neuroectodermal origin. In our cas e, the association with a medulloblastoma in a brother seems to confir m this concept.