CONGENITAL MICROANGIOPATHIC HEMOLYTIC-ANEMIA - A VARIANT OF THROMBOTIC THROMBOCYTOPENIC PURPURA

We describe a child with recurrent microangiopathic haemolytic anemia (MAHA) and thrombocytopenia (TCP) who presented on the first day of li fe. Remission was maintained only by regular infusions of fresh frozen plasma (FFP). This case shows similarities with others described in t he literature as examples of thrombotic thrombocytopenic purpura (TTP) , although the absence of renal or neurological involvement distinguis hes this disorder from classical TTP.