Tracheoesophageal fistula without atresia (H-type) is a known but unco
mmon cause of respiratory distress in the newborn. We present a rare c
ase of a high cervical tracheoesophageal fistula unassociated with a l
aryngeal cleft or esophageal atresia. The diagnosis, associated anomal
ies, and surgical repair of this previously undescribed entity are dis
cussed.