POLYSPLENIA SYNDROME AND CONGENITAL SHORT PANCREAS

We present a report of a stillborn female of mixed ancestry with conge nitally short pancreas, polysplenia, congenital heart defect, normal b ronchial branch pattern, and interruption of the inferior vena cava to add to the growing numbers (15) of this malformation complex in the l iterature. Additional manifestations were congenital hydrocephalus and absence of intestinal malrotation. A recent poster presentation at th e Second International Workshop on Fetal Genetic Pathology in Montana by Drut et al. underlined the importance of reporting these cases and of the pathological examination required [''Abnormal Spleen Lobulation and Short Pancreas,'' in Blastogenesis-Normal and Abnormal. New York: Wiley-Liss, Inc. for the National Foundation-March of Dimes, 1993]. ( C) 1993 Wiley-Liss, Inc.