S. Mar et C. Essex, TYPE-2 TRACHEAL AGENESIS WITHOUT TRACHEOESOPHAGEAL FISTULA, International journal of pediatric otorhinolaryngology, 39(2), 1997, pp. 159-161
Tracheal agenesis is a potentially lethal congenital anomaly first des
cribed by Payne in 1900 [1]. It can occur in isolation or in associati
on with tracheoesophageal (TO) or bronchoesophageal (BO) fistula, card
iovascular anomalies, limb deformities, vertebral anomalies and gastro
intestinal tract abnormalities [2]. There are 47 reported cases of tra
cheal agenesis up to 1989; 45 of these were associated with TO fistula
[2]. Another 15 cases of tracheal agenesis have been reported since t
hen, and all have been associated with TO fistula. We report only the
third case of type 2 tracheal agenesis without TO fistula. (C) 1997 El
sevier Science Ireland Ltd.