Fourteen occipitoatlantal dislocations were treated during an 11-year
period. All patients presented with neurological deficits and definite
evidence of spinal instability. Plain radiographs provided the diagno
sis conclusively in 11 patients. Three patients required computed tomo
graphy (CT) or magnetic resonance (MR) imaging for diagnosis. Rotation
al subluxations were radiographically occult and associated with less
severe neurological injuries compared to distracted or translated subl
uxations. Ten patients died acutely. One patient, who had complete C1
level quadriplegia, died after 3 months. Three patients with incomplet
e spinal cord syndromes had long-term survival and functional neurolog
ical recoveries. Extensive ligamentous injury predisposed patients to
recurrent subluxations. In several patients, traction or a cervical co
llar caused distraction and neurological injury. Halo immobilization a
nd urgent fusion are necessary for patients with salvageable neurologi
cal function. Nonoperative measures are inadequate for immediate or lo
ng-term spinal stability.